Background
Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, hereditary, sensory autonomic neuropathy. There are few reports on CIPA combined with Charcot spine. Operation is a most effective method for CIPA patients who combine with Charcot spine, but those patients are easy to get hyperthermia and internal fixation failure after operation. Patients’ deficit teeth also make nutrition management difficult. In order to help patients to avoid these problems, we designed a series of preoperative and postoperative nursing means: 1. Rectal temperature monitoring and Temperature control 2. Use new posture management 3. Assess the nutritional status of patients and make a diet plan. In this study, we aimed to evaluate the effect of these nursing means.
Methods
We retrospectively analysed the records of 3 CIPA patients combined with Charcot spine who accepted our nursing means to examine the effect of the nursing means.
Results
Rectal thermometry was more accurate than axillary thermometry. Physical cooling prevented hyperthermia for CIPA patients after operation. None of 3 patients had internal fixation failure. The BMI of one patient was only 14.0(malnutrition) before surgery, through nutritional intervention, all 3 patients’ serum albumin levels returned to normal before discharge from the hospital.
Conclusions
In summary, this study has made a lot of suggestions that can improve the prognosis of CIPA patients with Charcot spine.
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Posted 05 Jan, 2021
Posted 05 Jan, 2021
Background
Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, hereditary, sensory autonomic neuropathy. There are few reports on CIPA combined with Charcot spine. Operation is a most effective method for CIPA patients who combine with Charcot spine, but those patients are easy to get hyperthermia and internal fixation failure after operation. Patients’ deficit teeth also make nutrition management difficult. In order to help patients to avoid these problems, we designed a series of preoperative and postoperative nursing means: 1. Rectal temperature monitoring and Temperature control 2. Use new posture management 3. Assess the nutritional status of patients and make a diet plan. In this study, we aimed to evaluate the effect of these nursing means.
Methods
We retrospectively analysed the records of 3 CIPA patients combined with Charcot spine who accepted our nursing means to examine the effect of the nursing means.
Results
Rectal thermometry was more accurate than axillary thermometry. Physical cooling prevented hyperthermia for CIPA patients after operation. None of 3 patients had internal fixation failure. The BMI of one patient was only 14.0(malnutrition) before surgery, through nutritional intervention, all 3 patients’ serum albumin levels returned to normal before discharge from the hospital.
Conclusions
In summary, this study has made a lot of suggestions that can improve the prognosis of CIPA patients with Charcot spine.
Figure 1
Figure 2
Figure 3
Figure 4
Figure 5
Loading...