Background: The peripapillary staphyloma (PS) is a rare non-hereditary congenital optic disc dysplasia, which is generally unilateral and is likely to occur with poor vision. Fundus uncovered a large deeply excavated optic nerve head, retinal pigment epithelium changes at its edges and normal disc and retinal blood vessels in size and features.
Case presentation: This literature present a bilateral case of an especially congential peripaillary staphyloma (CPS), which the patient with esotropia and nystagmus was exposed to abnormality when she was only 5-month-old. Several interesting features are present in this patient.
Conclusions: Usually they have a large extent on visual loss. Thus, although extreme rare, an early detection, treatment and follow ups are necessary.
Keywords: Staphyloma; optic nerve; congenital