Background: Follicular dendritic cell sarcoma (FDCS) is a very rare malignant soft tissue tumor. About half of the cases occurred in lymph node, mostly around neck. The uncommon inflammatory variant of FDCS is an Epstein-Barr virus (EBV)-associated neoplasm. It was first introduced as Inflammatory pseudotumor-like FDC in 2001. Few cases had been found in liver and spleen as primary tumor. It mimicked the presentation of cholangiocarcinoma in this case and few had been reported as primary liver tumor yet.
Case report: We represent a 53-year-old man who was referred to our department with a liver tumor. The tumor was accidently found during health exam at lateral segment, which was suspected to be cholangiocarcinoma on Magnetic Resonance Imaging(MRI).
The liver segment was complete resected via laparoscopic hepatectomy. The tumor turned out to be inflammatory FDCS. The tumor specimen was margin free. No recurrence was detected at a 12-month follow-up
Clinical Discussion: Inflammatory FDCS often found in liver and spleen. Taiwan was EBV high-prevalence country, but the occurrence seemed not related. Current management as FDCS, with radiation therapy and chemotherapy if total resection was not feasible.
Conclusion: Inflammatory FDCS is a rare malignant tumor in abdomen. Complete resection represents favorable outcome.